Urothelial tumors of the bladder are a well-known pathology in adults. In children they are very rare and there are no defined guidelines about their management. We report the case of a 5-year-old boy who presented to our department with gross hematuria. Ultrasonography and cystoscopy with histological study showed a noninvasive low grade papillary urothelial carcinoma. The patient underwent a transurethral resection with no recurrence till date. Clinically, urothelial tumors of the bladder are mainly revealed by gross and painless hematuria. Definitive diagnosis is obtained by cystoscopy: endoscopic aspect is typical and transurethral biopsy allows the tumor’s grading and the elimination of other possible causes of tumor-like lesions. Transurethral resection is the main modality of treatment in children. Due to the significant recurrence rates, a close follow-up is mandatory. This can be done using ultrasonography or cystoscopy. The superiority of either technique is still not evident.