Neurofibromatosis Type 1 (NF1) is one of the most frequently-observed genetic diseases. NF1 patients are under the risk of Phaeochromocytoma that is secondary to NF1 gene mutation, vascular dysplasia, scoliosis, benign and malign cancer.In this study, we are presenting Neurofibromatosis Type-1 and Phaeochromocytoma in a 24-year-old female patient who was followed due to resistant hypertension.We can conclude that young patients who are followed due to resistant hypertension must be scanned for the Hereditary Phaeochromocytoma. This is extremely important in preventing important systemic symptoms and even deadly results.