Pan cake kidney is extremely rare fusion anomalies seen within the kidneys and constitutes only 2% of all the fusion renal anomalies. Usually asymptomatic or incidentally diagnosed pan cake kidney presents clinically only when it’s complicated. Various complications seen within it are pertaining to stasis of urine, mal rotation and short length of ureters. Mass lesion within the pan cake kidney is very rarely reported. However wilm’s tumour is most commonly seen malignancy within the pan cake kidney. Here, we report a case of 18 years old male presented with right iliac fossa pain with haematuria. On various imaging techniques, the probable diagnosis of mass lesion within the pan cake kidney was made. Partial nephrectomy was done and the lesion proved to be wilm’s tumour on histopathology. The patient is doing well on follow up.