Background

There is a rare genetic condition called Hutchinson-Gilford progeria syndrome that causes premature aging. Perioperative management of such cases is challenging and needs meticulous evaluation and monitoring.

Clinical description

This report discusses the successful anaesthetic management of a 9-year-old male child with Hutchinson–Gilford Progeria syndrome (HGPS), who was scheduled for an elective left orchidectomy at our hospital.

Management and outcome

The case was successfully managed under general anaesthesia with meticulous planning and vigilant intraoperative monitoring. We secured the airway with a ProSeal laryngeal mask airway and monitored the electrocardiogram, heart rate, blood pressure, oxygen saturation using pulse oximetry, and end-tidal carbon dioxide intraoperatively. The child was successfully extubated at the end of surgery.

Conclusions

Children with progeria present particular anesthetic challenges because of anatomical variations and possible multisystem involvement. For successful results, titrated anesthetic dosage, careful preoperative evaluation, and attentive intraoperative monitoring are necessary.